11 KB147 KB10 KB199220252002Ihan Hren, Natašaštevilka:1letnik:365 stranistr. 47-51ISSN:1318-2099COBISSID:14748121URN:URN:NBN:SI:doc-74IU1CMCenAssociation of Radiology and OncologyRadiology and oncology (Ljubljana)ChildDiagnosismaksilaMaksilarne novotvorbeMaxillary neoplasmsMiofibromatozaMyofibromatosisnovotvorbeotrociOtrokrak (medicina)SurgerytumorInfantile myofibromathosis of the maxilla| a case report|Background. Infantile myofibromatosis is a rare benign tumour in children. Itscharacteristic symptoms are firm masses in soft tissues, bones and visceralorgans, and its common locations are head and neck. Three forms are well known: solitary, multicentric and visceral myofibromatosis. All have excellent prognosis, except the last one that may be lethal. Spontaneous regression can occur. Case report. We present an unusual case of infantile myofibromatosis of the maxilla in an adolescent. Conclusions. The infantile myofibromatosis should be managed with special caution because of the differential-diagnostic similarity with fibrosarcoma, leomyosarcoma, and histiocytosisIzhodišča. Infantilna miofibromatoza je redek benigni tumor otrok. Značilne sočvrste mase v mehkih tkivih, kosteh ali notranjih organih. Pogosto se pojavlja na glavi in vratu. Poznane so tri oblike: solitarna, multicentrična in visceralna miofibromatoza. Zadnja oblika je lahko smrtna, ostale imajo odlično prognozo. Znana je spontana regresija. Prikaz primera. Opisan je manj značilen primer najstnika z obsežno solitarno miofibromatozo zgornje čeljustnice. Zaključki. Pri diagnosticiranju infantilne miofibromatoze je potrebna posebna pozornost zaradi diferencialno diagnostične podobnosti s fibrosarkomom, leomiosarkomom, histiocitozoTEXTznanstveno časopisjejournalsSlovenian National E-content AggregatorNational and University Library of SloveniaDruštvo radiologije in onkologije